先天性后鼻孔闭锁并额外鼻孔鼻腔畸形1例

李春苗, 李颖, 韩富根, 等. 先天性后鼻孔闭锁并额外鼻孔鼻腔畸形1例[J]. 临床耳鼻咽喉头颈外科杂志, 2024, 38(11): 1077-1080. doi: 10.13201/j.issn.2096-7993.2024.11.016
引用本文: 李春苗, 李颖, 韩富根, 等. 先天性后鼻孔闭锁并额外鼻孔鼻腔畸形1例[J]. 临床耳鼻咽喉头颈外科杂志, 2024, 38(11): 1077-1080. doi: 10.13201/j.issn.2096-7993.2024.11.016
LI Chunmiao, LI Ying, HAN Fugen, et al. One case of congenital choanal atresia with additional nostril nasal cavity malformation[J]. J Clin Otorhinolaryngol Head Neck Surg, 2024, 38(11): 1077-1080. doi: 10.13201/j.issn.2096-7993.2024.11.016
Citation: LI Chunmiao, LI Ying, HAN Fugen, et al. One case of congenital choanal atresia with additional nostril nasal cavity malformation[J]. J Clin Otorhinolaryngol Head Neck Surg, 2024, 38(11): 1077-1080. doi: 10.13201/j.issn.2096-7993.2024.11.016

先天性后鼻孔闭锁并额外鼻孔鼻腔畸形1例

  • 基金项目:
    国家区域医疗中心开放课题资助(No:NRMC0105)
详细信息

One case of congenital choanal atresia with additional nostril nasal cavity malformation

More Information
  • 本文报道河南省儿童医院收治的1例先天性后鼻孔闭锁并额外鼻孔鼻腔畸形患儿。女,43 d,因“生后喘憋伴张口呼吸、吃奶受限”为代主诉入院,入院后完善纤维鼻咽镜、CT、基因检测并结合体检结果,诊断为:双侧先天性后鼻孔膜性闭锁、先天性额外鼻孔鼻腔畸形、鼻腔狭窄,于全身麻醉下行鼻内镜下双侧后鼻孔成形术及左侧前鼻孔成形术。术后患儿术后恢复良好。
  • 加载中
  • 图 1  双侧鼻腔外面观

    图 2  鼻部CT水平位图

    图 3  纤维鼻咽镜下见双侧鼻腔内可见分隔,左侧鼻腔狭窄,双侧后鼻孔闭锁

    图 4  术后内镜下图

    图 5  术后2个月复查鼻咽镜

    图 6  术后3个月拔除扩张管

    图 7  术后10个月复查

  • [1]

    Maas AP, Strieth S, Send T. Clinical management of choanal atresia[J]. Laryngorhinootologie, 2024, 103(1): 25-34. doi: 10.1055/a-2160-2777

    [2]

    Maheshwaran S, Pookamala S, Vijay Pradap R, et al. Practical tips for surgical management of bilateral choanal atresia[J]. Indian J Otolaryngol Head Neck Surg, 2023, 75(Suppl 1): 768-773.

    [3]

    Shanmuganathan P, Chong DK. Accessory nostril associated with choanal atresia[J]. J Craniofac Surg, 2021, 32(8): 2845-2847. doi: 10.1097/SCS.0000000000007778

    [4]

    魏欣, 牟忠林, 林振群, 等. 额外鼻孔伴鼻后孔骨性闭锁1例[J]. 临床耳鼻咽喉头颈外科杂志, 2010, 24(2): 65-65. doi: 10.3969/j.issn.1001-1781.2010.02.017

    [5]

    Tomoum MO, Askar MH, Mandour MF, et al. Stentless mirrored L-shaped septonasal flap versus stented flapless technique for endoscopic endonasal repair of bilateral congenital choanal atresia: a prospective randomised controlled study[J]. J Laryngol Otol, 2018, 132(4): 329-335. doi: 10.1017/S0022215117002614

    [6]

    Kurosaka H. Choanal atresia and stenosis: Development and diseases of the nasal cavity[J]. Wiley Interdiscip Rev Dev Biol, 2019, 8(1): e336. doi: 10.1002/wdev.336

    [7]

    王蓬鹏, 唐力行, 杨小健, 等. 鼻内镜下改良黏膜瓣技术治疗新生儿及婴幼儿先天性后鼻孔闭锁[J]. 中华耳鼻咽喉头颈外科杂志, 2021, 56(7): 713-718. doi: 10.3760/cma.j.cn115330-20200812-00668

    [8]

    Wang PP, Tang LX, Zhang J, et al. Combination of the endoscopic septonasal flap technique and bioabsorbable steroid-eluting stents for repair of congenital choanal atresia in neonates and infants: a retrospective study. [J]. J Otolaryngol Head Neck Surg, 2021, 50: 51. doi: 10.1186/s40463-021-00535-9

    [9]

    向荣, 许昱. 鼻窦药物支架与口服激素治疗慢性鼻窦炎伴鼻息肉的围术期疗效和安全性比较研究[J]. 临床耳鼻咽喉头颈外科杂志, 2023, 37(11): 878-885. https://lceh.whuhzzs.com/article/doi/10.13201/j.issn.2096-7993.2023.11.005

    [10]

    Kotova EN, Vyazmenov EO, Bogomilsky MR. New ways of solving the problem of restenosis in the surgical treatment of congenital choanal atresia in children[J]. Vestn Otorinolaringol, 2020, 85(1): 45-47. doi: 10.17116/otorino20208501145

    [11]

    Moreddu E, Rossi ME, Nicollas R, et al. Prognostic factors and management of patients with choanal atresia[J]. J Pediatr, 2019, 204: 234-239. doi: 10.1016/j.jpeds.2018.08.074

    [12]

    Srivastava P, Kumar P. Supernumerary nostril: a rare anomaly[J]. Indian J Otolaryngol Head Neck Surg, 2023, 75(1): 840-842.

    [13]

    Labib A, Elshahat A. Supernumerary nostril: two years follow-up[J]. J Craniofac Surg, 2017, 28(4): e330-e333. doi: 10.1097/SCS.0000000000003577

    [14]

    Kong TH, Kim YH. Supernumerary nostril: formation of a large additional nasal cavity in an adult patient[J]. J Craniofac Surg, 2022, 33(1): e17-e18. doi: 10.1097/SCS.0000000000007857

    [15]

    Shanmuganathan P, Chong DK. Accessory nostril associated with choanal atresia[J]. J Craniofac Surg, 2021, 32(8): 2845-2847. doi: 10.1097/SCS.0000000000007778

    [16]

    关舒文, 刘殿全, 张庆丰. 儿童颜面管理与人工智能[J]. 临床耳鼻咽喉头颈外科杂志, 2023, 37(8): 658-661. https://lceh.whuhzzs.com/article/doi/10.13201/j.issn.2096-7993.2023.08.012

  • 加载中

(7)

计量
  • 文章访问数:  325
  • PDF下载数:  117
  • 施引文献:  0
出版历程
收稿日期:  2024-01-13
修回日期:  2024-04-08
刊出日期:  2024-11-03

目录