蜗神经缺陷患儿听觉植入相关问题

张治华; 陈见清

doi:10.13201/j.issn.2096-7993.2025.01.002

蜗神经缺陷患儿听觉植入相关问题

张治华^1,2,3, ,,
陈见清^1,2,3

- 1.
  上海交通大学医学院附属第九人民医院耳鼻咽喉头颈外科(上海，200011)
- 2.
  上海交通大学医学院耳科学研究所
- 3.
  上海市耳鼻疾病转化医学重点实验室

详细信息

作者简介:
专家简介: 张治华，医学博士，主任医师，硕士生导师，上海交通大学医学院附属第九人民医院耳鼻咽喉头颈外科行政副主任，医疗专长：人工听觉植入、小耳畸形功能重建、侧颅底外科诊疗。围绕侧颅底肿瘤和人工耳蜗植入，主持国家自然科学基金面上项目2项，以第一作者或通讯作者发表SCI论文12篇，总影响因子48.061分(单篇最高15.9分)。
社会任职：中华医学会耳鼻咽喉头颈外科学分会青委副主委(第12届)，中华医学会耳鼻咽喉头颈外科学分会小儿学组委员(第12、13届)，上海医学会耳鼻咽喉头颈外科学分会委员(第20届)，上海医学会耳鼻咽喉头颈外科学分会小儿学组委员(第19、20届)，上海医师协会耳鼻咽喉头颈外科学分会秘书，常委(第3届)

通讯作者: 张治华，E-mail：zhihua.zhang2015@aliyun.com

中图分类号: R764.35

收稿日期: 2024-11-29

刊出日期: 2025-01-03

Issues of auditory implant in children with cochlear nerve deficiency

ZHANG Zhihua^1,2,3, ,,
CHEN Jianqing^1,2,3

- 1.
  Department of Otolaryngology Head and Neck Surgery, Ninth People's Hospital Affiliated to Shanghai Jiao Tong University School of Medicine, Shanghai, 200011, China
- 2.
  Institute of Otology, School of Medicine, Shanghai Jiao Tong University
- 3.
  Shanghai Key Laboratory of Translational Medicine for Ear and Nose Diseases

More Information

Corresponding author: ZHANG Zhihua, E-mail: zhihua.zhang2015@aliyun.com

Received Date: 29 November 2024

Publish Date: 03 January 2025

摘要

摘要: 蜗神经缺陷(cochlear nerve deficiency，CND)指的是蜗神经纤细或者缺失，研究发现其在先天性感音神经性聋患者中发病率约为18%。发病机制尚不明确，听觉干预效果个体差异较大，本文就CND的相关问题进行探讨。
- 蜗神经缺陷 /
- 听觉植入
Abstract: Cochlear nerve deficiency(CND) is a rare inner ear malformation characterized by a hypoplastic or absent cochlear nerve, resulting in variable hearing loss or total deafness, depending on the quantity of nerve fibers present. About 18% of congenital hearing loss are associated with CND. It is a disease of uncertain cause. The outcome of auditory implant in CND patients varies widely. This article will discuss the related issues of CND.
- cochlear nerve deficiency /
- auditory implant

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图 1 CND患儿听觉植入策略选择

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参考文献(16)

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