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摘要: 炎症性肌纤维母细胞瘤(inflammatory myofibroblastic tumor，IMT)是一种间叶性软组织肿瘤，生物学特性多表现为交界性或低度恶性。该肿瘤是一种罕见的儿童期肿瘤，平均发病年龄10岁，婴幼儿更为罕见，其病因与发病机制目前尚不清楚。临床表现无特异性，其临床表现与肿瘤发生部位有关，当肿瘤占位对相邻器官产生压迫，会表现为疼痛及功能障碍。从目前文献报道来看，发病部位以消化、呼吸系统居多，也偶见泌尿生殖系统、头颈部及四肢，其发生于婴幼儿鼻咽部累及鼻腔，笔者尚未见国内外相关报道。本文报道1例累及婴幼儿鼻腔和鼻咽的巨大IMT，通过多个手术路径行等离子微创手术获得满意疗效，可为此类疾病的治疗提供参考。
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关键词:
- 炎症性肌纤维母细胞肿瘤 /
- 婴幼儿 /
- 微创手术
Abstract: Inflammatory myofibroblastic tumor (IMT) is a rare mesenchymal soft tissue tumor characterized by borderline or low-grade malignancy. It is rare childhood tumor with an average age of onset of 10 years old. It is even rarer in infants and toddlers, and the etiology and pathogenesis of this tumor are still unclear. The clinical presentation of IMT is non-specific and are related to the location of the tumor. When the tumor compresses adjacent organs, it can cause pain and functional impairment. According to the current literature, IMT is most commonly found in the digestive and respiratory systems, but also occasionally occur in the genitourinary system, head and neck, and limbs. At present, there have been no reports of nasopharyngeal IMT involving nasal cavity of infants and toddlers at home and abroad.This article reports a case of a massive inflammatory myofibroblastic tumor involving the nasal cavity and nasopharynx in an infant. Plasma-assisted minimally invasive surgery was performed through multiple surgical approaches and achieved satisfactory therapeutic results. This case report may provide valuable reference for the treatment of similar diseases.-
Key words:
- inflammatory myofibroblastic tumor /
- infant /
- minimally invasive surgery
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