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摘要: 尤文肉瘤（Ewing’s sarcoma,ES）是继骨肉瘤之后第二常见的原发性恶性肿瘤,占儿童恶性肿瘤的3%[1],主要影响躯干和长骨。在所有的ES患者中,只有1%～6%影响到颅骨、上颌骨、额骨、顶骨、筛骨或颞骨[2]。我院曾收治1例中年男性颞骨ES患者,现报告如下。1 病例报告患者,男,33岁,自诉入院10 d前吹风扇受凉后出现头痛,伴发热,最高39℃,3 d后出现右耳疼痛,7 d后出现右眼睑闭合不全,口角向左歪斜,伴头昏、耳Abstract: Ewing's sarcoma is a malignant, round cell tumor arising from the bones and primarily affecting children and adolescent. Involvement of the skull bones is rarely reported, constituting 1%-6% of the total Ewing's sarcoma cases. We describe a 33 years old male patient having Ewing sarcoma of the mastoid and petrous parts of temporal bone, whose clinical presentation mimicked mastoiditis with facial nerve palsy. We discuss the clinical and therapeutic course of an extensive primary Ewing sarcoma of the temporal bone and review this entity's literature in detail. The etiopathology of an acute peripheral facial palsy is often hard to identify. If the facial weakness starts together with symptoms suggesting an inflammatory process, the differential diagnosis may be focused first on diseases like herpes zoster oticus and a severe course of acute purulent otitis media. As an uncommon tumor of the temporal bone, physicians should consider Ewing's sarcoma in the differential diagnosis of children and adolescents who present with facial nerve paralysis. And in the case of ambiguous clinical findings, a surgical exposure of the middle ear is recommended.
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Key words:
- osteosarcoma /
- temporal bone /
- facial nerve paralysis
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