听觉及平衡系统损害的Cogan综合征2例

马妍佳; 汪芹; 伍伟景; 刘嘉; 丁艳

doi:10.13201/j.issn.1001-1781.2019.04.021

听觉及平衡系统损害的Cogan综合征2例

- 中南大学湘雅二医院耳鼻咽喉科(长沙, 410001)

详细信息

通讯作者: 汪芹,E-mail:455616210@qq.com

中图分类号: R764.4

收稿日期: 2018-09-05

Cogan syndrome with audiovestibular disfunction: 2 cases report

More Information

Corresponding author: WANG Qin, E-mail: 455616210@qq.com

Received Date: 05 September 2018

摘要

- Cogan综合征 /
- 听力损失 /
- 前庭功能
Abstract: We describe a case of Cogan syndrome in patients with clinical manifestations, related examinations and diagnosis, treatment, and review of relevant literature. Both patients had bilateral moderate to severe sensorineural hearing loss. The collateral function test showed that there were bilateral semicircular canal paresis, and the head impulse test had a bilateral gain value between 0.09 and 0.55. It showed obvious compensatory saccade wave, the head impulse suppression test bilateral no anti-compensation saccade wave. Cogan syndrome is a rare syndrome with unspecific symptoms and early diagnosis is difficult. However, the involvement of the auditory-vestibular systems are often poor prognosis and needs to be diagnosed by early diagnosis and treatment.
- Cogan syndrome /
- hearing loss /
- vestibular function

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