54例非综合征性前庭导水管扩大的临床分析

王利利; 宋云韬; 耿曼英; 米彦芳; 郭小艳; 王蕾; 汤建芬; 李仲; 李文超

doi:10.13201/j.issn.1001-1781.2019.03.017

54例非综合征性前庭导水管扩大的临床分析

- 郑州大学第二附属医院耳鼻咽喉头颈外科(郑州, 450014)

详细信息

通讯作者: 耿曼英,E-mail:manying66@126.com

中图分类号: R764.43

收稿日期: 2018-10-16

Clinical analysis of 54 patients with non-syndromic enlarged vestibular aqueduct

- Department of Otolaryngology Head and Neck Surgery, the Second Affiliated Hospital of Zhengzhou University, Zhengzhou, 450014, China

More Information

Corresponding author: GENG Manying, E-mail: manying66@126.com

Received Date: 16 October 2018

摘要

摘要: 目的:进一步认识非综合征性前庭导水管扩大的临床特点,为临床诊治提供参考。方法:收集54例临床上确诊为非综合征性前庭导水管扩大病例,通过病史询问、体格检查、听力学及影像学检查,分析其临床特点,测量颞骨高分辨率薄层CT轴位上前庭总脚至前庭导水管外口之间中点的最大管径宽度,应用t检验分析其与耳侧别、听力下降类型及听力下降程度的关系。结果:54例非综合征性前庭导水管扩大患者均双侧耳受累,语前聋42例,语后聋12例;38耳为重度聋,70耳为极重度聋;听力下降类型96耳表现为感音神经性聋,12耳为混合性聋;前庭总脚至前庭导水管外口之间中点的最大管径宽度为1.60~3.90mm,平均2.60mm;左右侧耳、听力损失程度、听力损失类型组间数据差异均无统计学意义。结论:非综合征性前庭导水管扩大主要表现为较重的感音神经性聋,其诊断依靠影像学检查,扩大程度左右侧无差异,且与听力下降程度及类型无相关性。
- 前庭导水管扩大 /
- 聋 /
- 高分辨率CT /
- 核磁共振
Abstract: Objective:To further recognize the clinical characteristics of non-syndromic enlarged vestibular aqueduct through the retrospective analysis of cases, with the purpose of providing references for clinical diagnosis and treatment.Method:Collect 54 cases of non-syndromic enlarged vestibular aqueduct, and analyze their clinical characteristics after history taking, physical examination, audiometry and imaging examination.Measure the biggest width of midpoint between internal and external of vestibular aqueduct on temporal bone thin-section CT, and analyze the relationship between the pipe width and sides of ear, types of hearing loss and degree of hearing loss through t test.Result:All 54 patients with non-syndromic enlarged vestibular aqueduct had bilateral ear involvement.There were 42 cases with prelingual deafness, 12 cases with postlingual deafness, and there were 38 ears with severe deafness, 70 ears with profound deafness.Ninety-six ears of hearing loss showed sensorineural deafness, and 12 ears manifested mixed deafness.The biggest width of midpoint between internal and external of vestibular aqueduct spread over 1.60-3.90 mm, and the average was 2.60 mm.There were no significant differences in data between left and right sides, degree of hearing loss and type of hearing loss.Conclusion:Non-syndromic enlarged vestibular aqueduct mainly manifests serious sensorineural deafness, and the diagnosis depends on imaging examination.There is no difference in the degree of expanding between left and right ear, and the extent of enlargement is not related to the type and the severity of hearing loss.
- enlarged vestibular aqueduct /
- deafness /
- HRCT /
- MRI

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