儿童单侧聋的发现途径及病因分析

梅玲; 陈向平; 杨军

doi:10.13201/j.issn.1001-1781.2018.16.010

儿童单侧聋的发现途径及病因分析

- 上海交通大学医学院附属新华医院听力障碍和眩晕诊治中心(上海, 200092)

详细信息

通讯作者: 梅玲,E-mail:meiling@xinhuamed.com.cn

中图分类号: R764.43

收稿日期: 2018-06-11

The study of detection and etiology of unilateral deafness in children

- Hearing and Vertigo Center, Xinhua Hospital, Medical School of Shanghai Jiaotong University, Shanghai, 200092, China

More Information

Corresponding author: MEI Ling, E-mail: meiling@xinhuamed.com.cn

Received Date: 11 June 2018

摘要

摘要: 目的：探讨儿童单侧聋的发现途径及病因，为临床诊断、治疗提供依据。方法：回顾性分析36例单侧聋儿童的病史、颞骨薄层CT和内听道MRI检查结果，分析儿童单侧聋的发现途径及影像学评估结果。结果：儿童单侧聋的平均诊断年龄是6周岁，经新生儿听力筛查发现的患儿平均诊断年龄是7.7月龄。80.6%的患儿有内耳畸形，其中96.6%的患儿蜗神经发育不良，占总研究人数的77.8%。结论：新生儿听力筛查可早期发现儿童单侧聋。蜗神经发育不良是儿童单侧聋的主要病因。内听道MRI应作为儿童单侧聋的首选影像学检查。
- 聋 /
- 新生儿 /
- 听力筛查 /
- 耳蜗神经
Abstract: Objective: To explore the detection approach and aetiology of single-side deafness(SSD) in children and provide evidence for diagnoses and treatment.Method: A retrospective study was performed. Medical history and radiological data of children with unilateral deafness were analyzed.Result: The mean age at diagnosis was 6 years old. The mean age at diagnosis was 7.7 month because of failure of universal newborn hearing screening. Inner ear malformations were identified in 80.6% of cases. Cochlear nerve deficiency(CND) was observed in almost 77.8% of our cases, accounts for 96.6% in children with inner ear malformations.Conclusion: The children with SSD could be early detected by UNHS. CND is the main aetiology for SSD. MRI should be the first image choice when SSD children was diagnosed.
- deafness /
- neonate /
- hearing screening /
- cochlear nerve

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