婴幼儿听神经病谱系障碍与人工耳蜗植入研究进展

陈婧媛; 李永新

doi:10.13201/j.issn.1001-1781.2018.14.020

婴幼儿听神经病谱系障碍与人工耳蜗植入研究进展

陈婧媛,
李永新^,

- 首都医科大学附属北京同仁医院耳鼻咽喉头颈外科, 耳鼻咽喉头颈科学教育部重点实验室(首都医科大学)(北京, 100730)
基金项目:
首都卫生发展科研专项（No：2016-1-5014）；北京市科委首都临床特色应用研究项目（No：Z161100000516103）；国家自然科学基金（No：81670923）

详细信息

通讯作者: 李永新,E-mail:entlyx@sina.com

中图分类号: R764.4

收稿日期: 2018-03-08

Research progress on auditory neuropathy spectrum disorder and cochlear implantation in infants and young children

CHEN Jingyuan,
LI Yongxin^,

More Information

Corresponding author: LI Yongxin, E-mail: entlyx@sina.com

Received Date: 08 March 2018

摘要

- 听神经病谱系障碍 /
- 人工耳蜗植入
Abstract: Auditory neuropathy is a disorder characterized by absent or severely abnormal auditory brainstem response (ABR) with intact outer hair cell function, as evidenced by the presence of evoked otoacoustic emissions and/or cochlear microphonics. Unlike patients with sensory hearing loss who show clinical evidence of impaired outer hair cell function. For ANSD patients, clinical rehabilitation is mainly limited to hearing aid wearing and cochlear implantation. However, the effect of cochlear implantation for ANSD patients may be difference. The outcome of cochlear implantation is related to the lesion location, the age of implantation and the diameter of cochlear nerve.
- auditory neuropathy spectrum disorder /
- cochlear implant

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参考文献(50)

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