上颌窦恶性横纹肌样瘤1例

罗扬拓; 施磊; 姜学钧

doi:10.13201/j.issn.1001-1781.2016.19.018

上颌窦恶性横纹肌样瘤1例

- 中国医科大学附属一院耳鼻咽喉科(沈阳, 110001)

详细信息

通讯作者: 姜学钧,E-mail:drjxj@163.com

中图分类号: R739.62

收稿日期: 2016-04-17

Malignant rhabdoid tumor of the maxillary sinus:a case report

More Information

Corresponding author: JIANG Xuejun, E-mail: drjxj@163.com

Received Date: 17 April 2016

摘要

- 鼻肿瘤 /
- 恶性横纹肌样瘤 /
- 鼻出血
Abstract: Malignant rhabdoid tumors(MRTs)are most commonly found in the kidneys of young children,and the prognosis is very poor.Here,we present a case of primary MRT of the maxillary sinus,which is an extremely rare and scarcely been reported.A 56-year-old male complained of repeated epistaxis for over 1 year duration.CT scan showed soft tissue density in the paranasal sinus,and no obvious bone resorption or damage was observed.The patient underwent endoscopic sinus surgery.Postoperative biopsy showed undifferentiated malignant neoplasm with features of rhabdoid differentiation.Immunohistochemistry(IHC)was positive for the expression of vimentin but negative for desmin,pan CK and S-100.Histopathological examination and IHC analysis supported the diagnosis of MRT.
- nose neoplasms /
- malignant rhabdoid tumor /
- epistaxis

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参考文献(2)

[1]

BRENNAN B,STILLER C,BOURDEAUT F,et al.Extracranial rhabdoid tumours:what we have learned so far and future direction[J].Lancet Oncol,2013,14:e329-336.

[2]

DEISCH J,RAISANEN J,RAKHEJA D.Immunohistochemical expression of embryonic stem cell markers in malignant rhabdoid tumors[J].Pediatr Dev Pathol,2011,14:353-359.

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