先天性内耳畸形的影像学及听力学分析

周宝; 林少莲; 林有辉; 方哲明; 叶胜难; 张榕

doi:10.13201/j.issn.1001-1781.2015.22.005

先天性内耳畸形的影像学及听力学分析

- 福建医科大学附属第一医院耳鼻咽喉头颈外科(福州, 350005)

详细信息

通讯作者: 叶胜难; 张榕,E-mail:zhang2012rong@sina.cn

中图分类号: R764.43

收稿日期: 2015-09-16

Imaging and audiology analysis of the congenital inner ear malformations

- Department of Otorhinolaryngology Head and Neck Surgery, the First Affiliated Hospital of Fujian Medical University, Fuzhou, 350005, China

More Information

Corresponding authors: YE Shengnan ; ZHANG Rong

Received Date: 16 September 2015

摘要

摘要: 目的: 研究感音神经性聋患儿的颞骨影像学及听力学表现,分析内耳畸形的类型及其发生率。方法: 对确诊为感音神经性聋患儿行颞骨CT和内耳水成像检查,对影像学及听力学表现进行回顾性分析。结果: 590例感音神经性聋患儿中125例(232耳)存在内耳发育畸形。重度聋以上患耳的内耳畸形率约占21.71%,中度聋以下患耳的内耳畸形率12.85%。听力正常耳的内耳畸形率13.59%。结论: 颞骨CT及MRI检查对了解内耳畸形有重要意义。内耳畸形多为双侧,听力损失多为极重度,耳蜗前庭畸形、前庭水管扩大较为常见。感音神经性聋患儿中,重度聋以上患耳的内耳畸形率较中度聋以下患耳的内耳畸形率高,听力正常耳亦可存在内耳畸形。
- 感音神经性聋 /
- 内耳畸形 /
- 先天性 /
- CT /
- MRI
Abstract: Objective: To investigate imaging and audiology features of temporal bone and analyze the classification and prevalence of inner ear abnormalities in children with sensorineural hearing loss.Method: Children who were diagnosed with sensorineural hearing loss were examined by high resolution CT and the inner ear fluid of MRI.And each chart was retrospectively reviewed to determine the imaging and audiology features.Result: There were 125 patients(232 ears) found with inner ear malformation in 590 children with SNHL. About 21.71% of the inner ear malformation occurred in severe and profound hearing loss ears, and 12.85% occurred in r moderate hearing loss ears. The inner ear malformation rate in normal hearing ears were 13.59%.Conclusion: CT and MRI examinations of temporal bone are important diagnostic tools to indentify inner ear malformations. Inner ear malformations are almost bilateral and hearing loss are profoud. Cochleovestibular malformations and large vestibular aqueduct are the 2 most frequent deformities. Among the children with SNHL,deformity rate in the severe and profound hearing loss ears is higher than that in moderate hearing loss ear. Inner ear malformations can exist in people with normal hearing.
- sensorineural hearing loss /
- inner ear malformations /
- congenital /
- CT /
- MRI

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