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Abstract: Primitive neuroectodermal tumor(PNET)is a small round cell malignancies,normally confined to the chest wall and soft tissues of children and young adults,and reports of this tumor existing in nasal cavity are scarce.We herein present a case of nasal PNET.A 35-year-old male patient presented with a chief complaint of stuffy nose was diagnosed with a primary nasal pPNET by the clinical,microscopic,immunohistochemical features.Since these tumors are highly aggressive and patient prognosis is typically very poor,early diagnosis,immediate surgical resection and re-resection if possible,early radiotherapy and chemotherapy and close follow-up are required.We also review literatures on pPNET.
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Key words:
- nasal /
- primitive neuroectodermal tumor
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