岩骨胆脂瘤临床特点及诊治分析

张绍兴, 马芙蓉, 李哲生, 等. 岩骨胆脂瘤临床特点及诊治分析[J]. 临床耳鼻咽喉头颈外科杂志, 2013, 27(19): 1058-1062,1067. doi: 10.13201/j.issn.1001-1781.2013.19.011
引用本文: 张绍兴, 马芙蓉, 李哲生, 等. 岩骨胆脂瘤临床特点及诊治分析[J]. 临床耳鼻咽喉头颈外科杂志, 2013, 27(19): 1058-1062,1067. doi: 10.13201/j.issn.1001-1781.2013.19.011
ZHANG Shaoxing, MA Furong, LI Zhesheng, et al. Clinical analysis of petrous bonecholesteatoma:characteristics,diagnosis and treatment[J]. J Clin Otorhinolaryngol Head Neck Surg, 2013, 27(19): 1058-1062,1067. doi: 10.13201/j.issn.1001-1781.2013.19.011
Citation: ZHANG Shaoxing, MA Furong, LI Zhesheng, et al. Clinical analysis of petrous bonecholesteatoma:characteristics,diagnosis and treatment[J]. J Clin Otorhinolaryngol Head Neck Surg, 2013, 27(19): 1058-1062,1067. doi: 10.13201/j.issn.1001-1781.2013.19.011

岩骨胆脂瘤临床特点及诊治分析

  • 基金项目:

    北京大学第三医院临床学科重点项目 (No:62450-6)

    卫生部国家临床重点专科 (No:62450-10)

详细信息
    通讯作者: 马芙蓉,E-mail:furongma@126.com
  • 中图分类号: R764

Clinical analysis of petrous bonecholesteatoma:characteristics,diagnosis and treatment

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  • 目的:探讨颞骨岩骨部胆脂瘤的临床表现特点、诊断和治疗。目的:对我科收治的随访资料完整的12例岩骨胆脂瘤(PBC)患者进行回顾性分析。结果:①7例主要表现为长期耳流脓史伴听力下降,后期有面瘫、重度听力下降、眩晕发作;与慢性中耳炎病史及耳科手术史密切相关。另外5例,其病程隐匿,临床表现早期不以流脓为主,后期可有此表现;初诊以面瘫、严重的感音神经性聋或混合性聋,甚至眩晕发作等症状为主;②11例有不同程度的面神经功能损失,多数为Ⅳ~Ⅵ级;破坏累及耳蜗10例,内听道9例,半规管11例;10例选择经迷路-耳蜗(耳囊)入路手术,其余2例迷路入路手术;1例术中借助内镜;4例术中行颞骨次全切除,术腔填塞、耳道咽鼓管封闭术;随访3例复发,行二次手术;其余9例无复发。6例行面神经吻合,面神经功能由House BrackmannⅤ~Ⅵ级恢复到Ⅲ~Ⅳ;3例面神经减压,由Ⅳ~Ⅴ恢复到Ⅱ~Ⅲ级。结论:岩骨胆脂瘤病史中具有引起重度耳聋、面瘫的特点,先天性者病程隐匿,危害更甚;治疗原则为彻底去除病变,尽量保留功能。选择手术径路需考虑病变范围和听力状况,硬脑膜缺损、脑脊液漏时可选用颞骨次全切除术,病变深在,切除困难时,可借助内镜扩大视野。
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出版历程
收稿日期:  2013-07-13

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